A rare, bilateral, autosomal dominant disorder of the Descemet’s membrane and corneal endothelium,. It is marked by non-inflammatory corneal opacities, vesicle-like lesions, or subtle band-like lesions that can lead to edema of the stroma and affect vision. It is divided into two types; PPMD (CHED type 1), which presents after the first year of life, and CHED type 2, which presents immediately after birth.
Also Known As
- Schlichting Dystrophy
- Posterior Polymorphous Corneal Dystrophy