A rare, bilateral, slow-progressing disease characterized by several small granules resembling crumbs in the superficial central corneal stroma in people aged 40 and above. Unlike Type 1, Type II manifests without recurrent corneal erosions and has fewer deposits. It is an autosomal dominant inherited disease of the TGFBI gene on the 5q31 locus.

Also Known As

  • Granular-Lattice Dystrophy