A sporadic eye condition where the cell layer lining the corneal interior multiplies rapidly, resulting in the swelling of the cornea (edema), iris distortion and elevated intraocular pressure (glaucoma). The disorder mostly affects middle-aged women and is among the three syndromes that constitute the iridocorneal endothelial syndrome (ICE syndrome). The other two are Cogan-Reese syndrome and progressive iris atrophy.

Also Known As

  • Iridocorneal Endothelial Syndrome
  • Iris Atrophy with Corneal Edema and Glaucoma